Submission Details

Submitter:

Classification:
Definitive
GENCC:100001
Gene:
Disease:
branchio-oto-renal syndrome
Mode Of Inheritance:
Autosomal dominant
Evaluated Date:
11/21/2017
Evidence/Notes:

The EYA1 gene has been associated with autosomal dominant Branchio-oto-renal syndrome using the ClinGen Clinical Validity Framework as of 10/17/17. This association was made using case-level data. Multiple missense, nonsense, frameshift and splice-site variants have been reported in humans. EYA1 was first associated with this disease in humans as early as 1997 (Abdelhak et al.

PubMed IDs:
10072433 11734542 14628042 18220287 19206155 19951260
Public Report:
Assertion Criteria:
Submitter Submitted Date:
12/05/2025

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